Quinticuspid aortic valve causing aortic valve incompetence and stenosis.

Aortic valve dysfunction may be the consequence of congenital malformation of the aortic valve. Unicuspid,'2 bicuspid,'-6 tricuspid,23 and quadricuspid68 aortic valves have all been described. We describe a patient who presented with cardiac enlargement caused by aortic valve incompetence and stenosis. Echocardiograms repeatedly showed multiple closing lines in the aortic valve orifice. This patient was found to have a quinticuspid aortic valve; the left coronary and non-coronary cusps were normal in size, and the remainder of the valve consisted of three small cusps divided by well-developed commissures.